Pyoderma Gangrenosum
Features
typically on the lower limbs
initially small red papule
Progresses to deep, red, necrotic ulcers with a violaceous border
Systemic symptoms (malaise, fever, myalgia)
Causes*
idiopathic (50%)
inflammatory bowel disease (UC, Crohn's
rheumatoid arthritis, SLE
myeloproliferative disorders
lymphoma, myeloid leukaemias
monoclonal gammopathy (IgA)
primary biliary cirrhosis
Management
First line
Oral corticosteroids
Second line
ciclosporin
infliximab
page revision: 0, last edited: 16 Feb 2017 08:27